General Practice 2022

SíEvans syndrome: what é, symptoms, causes and treatment

Table of contents:

SíEvans syndrome: what é, symptoms, causes and treatment
SíEvans syndrome: what é, symptoms, causes and treatment

Evans syndrome, also known as antiphospholipid syndrome, is a rare autoimmune condition in which the body produces antibodies that destroy blood.

Some people with this syndrome may have only destroyed white cells, only red cells or only platelets, but in general, the entire structure of the blood is altered, leading to the appearance of anemia or other characteristic symptoms such as easy bruising or bleeding.

The sooner the correct diagnosis of the syndrome is made, the easier it is to control the symptoms and thus the person can have a better quality of life.

Main signs and symptoms

When red blood cells are damaged, lowering their blood levels, the patient develops the typical symptoms of anemia, with pallor, easy tiredness or headache.

In cases where platelets are to be destroyed, the patient is more susceptible to bruising and bleeding. When it is the white portion of the blood that is affected, the patient is more susceptible to infections, in addition to having greater difficulty in recovering from diseases.

It is common for people with Evans syndrome to also have other autoimmune diseases, such as lupus or rheumatoid arthritis, for example.

What causes the syndrome

The factor that promotes this syndrome is still unknown, and both the symptoms and the course of this disease are very different from one case to another, depending on the portion of the blood that is affected.

How the treatment is done

The treatment aims to stop the production of antibodies that destroy blood cells. Treatment does not cure the disease, but it helps to reduce its symptoms, such as anemia or thrombosis.

The use of steroids is recommended as they suppress the immune system and decrease the production of antibodies, decreasing the degree of destruction of blood cells.

Another option is the injection of immunoglobulins to destroy the excess antibodies produced by the body or even chemotherapy, which stabilizes the patient. In more severe cases, removal of the spleen is another form of treatment, as well as blood transfusion.

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